Idiopathic Pulmonary Fibrosis and Progressive Pulmonary Fibrosis - Clinical Practice Guideline

This clinical practice guideline document from the American Thoracic Society, European Respiratory Society, Japanese Respiratory Society, and Asociacion Latinoamericana de Torax updates prior guidelines for idiopathic pulmonary fibrosis (IPF) and addresses the progression of pulmonary fibrosis in patients with interstitial lung diseases (ILDs) other than IPF.

The guidelines include, but are not limited to:

• Diagnosing and treating IPF
• The radiological features of usual interstitial pneumonia (UIP), the hallmark of IPF
• The histopathological features of UIP used in diagnosis
• Evidence-based recommendations for diagnosing IPF
• Updates to the 2018 guidelines for diagnosing IPF
• Evidence-based recommendations for the treatment of IPF
• The diagnosis and treatment of PPF in fibrotic ILD, including a definition of PPF
• Physiological criteria for PPF
• Radiological criteria for PPF
• Evidence-based recommendations for the treatment of PPF